Eight patients with sunct syndrome underwent a 4week, openlabel, daily treatment with 600900 mg gbp. Diagnosis and treatment of this condition are challenging. Pain syndromes that may mimic sunct headache include cluster headache, temporal arteritis, trigeminal neuralgia involving the first division of the trigeminal nerve, demyelinating disease, primary stabbing headache, hypnic headache, and chronic paroxysmal. On a good day i might just have 34, but the worst ive had was more like 70 in a day. I cant remember that my boss was a trigger for sunct attacks.
Therefore, its differential diagnosis and treatment are challenging and disputable. Symptoms include excruciating burning, stabbing, or electrical headaches mainly near the eye. The syndrome has been described more fully over subsequent years sjaastad et al. The case we report here involves a woman whose symptoms were brought on by a dietary. Opalski syndrome is a rare variation of lateral medullary syndrome lms accompanied by ipsilateral hemiparesis. Hemicrania continua hc, paroxysmal hemicrania ph and short lasting neuralgiform headache attacks sunct and suna are rare syndromes with a difficult therapeutic approach. A version of this article was copy edited by despayre, a member of the guild of copy editors, on march 4, 2012. Sunct syndrome associated with compression of trigeminal nerve. Shortlasting unilateral neuralgiform headache attacks with conjunctival injection and tearing sunct is a rare but disabling primary headache disorder characterized by brief, severe, ipsilateral, orbitotemporal pain with autonomic features such as conjunctival injection, tearing, and rhinorrhea. The reported sunct patient is the first who responded to a combination treatment of oxcarbazepine and gabapentin. Shortlasting unilateral neuralgiform headache attacks with. Sunct syndrome successfully treated with the combination of oxcarbazepine and gabapentin sunct syndrome successfully treated with the combination of oxcarbazepine and gabapentin marziniak, martin. The guild welcomes all editors with a good grasp of english and wikipedia s policies and guidelines to help in the drive to improve articles. All papers published in english or german were considered when they described a controlled trial or a case series on the treatment of at least.
Although intravenous lidocaine can be used as a transitional treatment until beneficial effects of a preventive treatment becomes evident. Shortlasting, unilateral, neuralgiform headache attacks with conjunctival injection and tearing sunct syndrome is a rare headache. Shortlasting unilateral neuralgiform headache with conjunctival injection and tearing syndrome is a rare condition hardly ever encountered by those dealing with pain and may be confused with other pain types with autonomic origin. The pain is described as throbbing, sharp or stabbing. It is characterized by shortlasting unilateral attacks of severe neuralgiform pain associated. A set of diagnostic criteria of sunct syndrome is also given. The disorder is marked by bursts of moderate to severe burning, piercing, or throbbing pain, usually on one side of the head and around the eye or temple. After treatment onset, he experienced intense and pulsatile headache episodes. Headache in sunct universitair pijn centrum maastricht.
At around 30, this male patient had developed cycles of unilateral, ocularperiorbital, mostly lowgrade pain sjaastad et al 1978. Sunct syndrome has been previously described in association with lms. Here, we describe the case of a woman with shortlasting unilateral neuralgiform attacks with cranial autonomic symptoms suna. The headache seemed rather stable at this level until he, at 58, was struck by the end of a fishing rod in the lower, medial, supraorbital area on the symptomatic side. Results for sunct syndrome 1 8 of 8 sorted by relevance date click export csv or ris to download the entire page or use the checkboxes to select a subset of records to download export csv export ris 10 per page 50 per page 100 per page 250 per page. Trauma, arteriovenous malformations and pituitary adenomas may have a causative role. Sunct syndrome in two patients with prolactinomas and bromocriptineinduced attacks.
This page includes the following topics and synonyms. Paroxysmal hemicrania often the result of cervical pressure sunct syndrome, sjaastad syndrome, ion, on, gpn, etc. Clinical description the disease manifests with strictly unilateral pain attacks of moderatetosevere intensity. Sunct shortlasting, unilateral, neuralgiform headache attacks with conjunctival injection and tearingis a rare form of headache that is most common in men after age 50. The intense pain is typically localized at the distribution of the first division. It usually involves the ophthalmic division of the trigeminal nerve but, rarely, it may involve any part of the head. Primary res appears to have a frequent association with primary headaches especially migraine. The present report describes a sunct syndrome in a 64yearold male who had been diagnosed with trigeminal neuralgia several years ago.
Shortlasting unilateral neuralgiform headaches with conjunctival injection and tearing sunct is a rare headache syndrome which belongs to the trigeminal autonomic cephalalgias. Sunct headache is a clinical diagnosis supported by a combination of clinical history, normal physical examination, radiography, and mri. Shortlasting unilateral neuralgiform headache with conjunctival injection and tearing sunct is classified by the international headache society as a primary headache disorder. Red ear syndrome res is characterised by attacks of unilateral or bilateral burning ear pain associated with erythema. In sunct, pain paroxysms are typically periorbital, are extremely frequent up. New on here and have complicated sunct im tony, im 35, i have been getting the headaches everyday for about a year, and the amount varies but averages about 20 a day. Genetic and rare diseases information center gard po box 8126, gaithersburg, md 208988126 tollfree. Patients report brief attacks of unilateral, stabbing and throbbing headache lasting between 5 and. Matharu senior lecturer and honorary consultant neurologist, headache group, institute of neurology and the national hospital for neurology and neurosurgery, queen square, london, wc1n 3bg, uk 1 g. Efficacy of gabapentin in the treatment of sunct syndrome. Sunct syndrome treated with gamma knife targeting the trigeminal nerve and sphenopalatine ganglion, the journal of headache and pain, 2012, pp.
Sunct syndrome shortlasting unilateral neuralgiform. Shortlasting unilateral neuralgiform headache attacks. Sunct syndrome risks, symptoms and leading causes treato. As such, sunct and cluster headaches are sometimes grouped together as trigeminal autonomic cephalgias. The attacks are strictly unilateral, generally with the pain persistently confined to the ocularperiocular area. Chairman and professor of oral and maxillofacial surgery. Sunct syndrome is one of a number of trigeminal autonomic cephalalgias characterized by shortlasting headache occurring in the first division of the trigeminal nerve 2,3. If you do not see its contents the file may be temporarily unavailable at the journal website or you do not have a pdf plugin installed and enabled in your browser. Sunct syndrome treated with gamma knife targeting the. Sunct syndrome successfully treated with topiramate. The cause of sunct is unknown, but some think it involves a disturbance in a particular part of the brain, which may also involve the trigeminal nerve.
This means that sunct syndrome, or a subtype of sunct syndrome, affects less than 200,000 people in the us population. The pain is maximal in and around the eye and may radiate to the ipsilateral forehead, temple, nose, cheek, and palate 4. Medical treatment options include lamotrigine, topiramate. Sunct headache information page national institute of. Shortlasting unilateral neuralgiform headache with. It can be distinguished from other closely similar primary headaches because of the usually very brief attack duration 15120 seconds which can.
This article includes discussion of sunct, shortlasting unilateral neuralgiform. Suna shortlasting unilateral neuralgiform headache attacks with cranial autonomic symptoms. Despite a myriad of therapeutic trials, no convincingly effective remedy for sunct and suna is available at present. We describe one case of sunct syndrome secondary to consumption of. If you have questions, please direct them to our talk page. Since this initial description approximately 100 cases have been reported in the literature 25. Sunct emerges as a fairly clearcut, clinical syndrome. Symptoms are brought on by touch, exertion, heat or cold, stress, neck movements and washing or brushing of hair. Sunct headache genetic and rare diseases information. Although rarely seen, clinical status may be a feature of the sunct syndrome. Sunct shortlasting unilateral neuralgiform headache attack with. This case demonstrates the effectiveness of resection as definitive treatment for sunct syndrome associ ated with tumoral compression of the trigeminal nerve. S hortlasting unilateral neuralgiform headache attacks with conjunctival injection and tearing syndrome is a rare headache disorder classified under tac.
Sunct syndrome successfully treated with the combination. Frontiers comorbid sunct syndrome and opalski syndrome. Sunct syndrome, sunct headache, shortlasting unilateral neuralgiform headache attacks with conjunctival injection or tearing, suna headache, shortlasting unilateral neuralgiform headache attacks with cranial autonomic symptoms. Pathogenesis, surgical treatment, and cure for sunct syndrome. Red ear syndrome precipitated by a dietary trigger. If the address matches an existing account you will receive an email with instructions to retrieve your username. Suna, sunct, red ear syndrome, trigeminal autonomic cephalalgias, cranial autonomic symptoms background red ear syndrome res is a rare condition originally described by lance 1. Sunct, like cluster headache, is a primary headache disorder characterized by unilateral pain in the trigeminal nerve distribution and by autonomic manifestations. Sunct syndrome is listed as a rare disease by the office of rare diseases ord of the national institutes of health nih. Sunct syndrome and seborrheic dermatitis associated with craneosynostosis. For language access assistance, contact the ncats public information officer.
Sunct syndrome in association with persistent horner syndrome in a chinese patient. Shortlasting, unilateral, neuralgiform headache attacks with conjunctival injection and tearing sunct syndrome and tumor of. The first sunct patient was observed in 1977, at 62 years of age. Short lasting unilateral neuralgiform headache attacks with conjuntival injection and tearing sunct also manifests itself as a onesided headache and is associated with the autonomic symptoms as described in cluster headache ch. The patient was followed under lamotrigine treatment for 6 months and was symptom free during that period. Sunct syndrome is an acronym for shortlasting unilateral neuralgiform headache with conjunctival injection and tearing, it is a type of painful headache that is characterized as one sided and usually around the eye area. Report of a case and treatment update cosme gayescoda 1, gemma mayorsubirana 2, octavi campsfont 3, leonardo beriniaytes 4 1 md, dds, ms, phd. Sunct, pathophysiology, treatment, and trial last search in january, 2005. Red ear syndrome is a rare condition characterized by episodic attacks of erythema of the ear accompanied by burning ear pain. The patient reported stabbing pain in the orbital zone and in the left upper maxillary region, of great intensity, brief duration, and a frequency of 20100 attacks a day. The patient reported stabbing pain in the orbital zone and in the left upper maxillary region, of great intensity, brief duration, and a. If you have problems viewing pdf files, download the latest version of adobe reader. Friends, employers, and colleagues cluster headache. Introduction shortlasting unilateral neuralgiform headache attacks with conjunctival injection and tearing sunct is a rare primary headache syndrome first described in 1978 sjaastad et al.
A few cases of sunct syndrome have been reported in children. If you have problems viewing pdf files, download the latest version of adobe reader for language access assistance, contact the ncats public information officer genetic and rare diseases information center gard po box 8126, gaithersburg, md 208988126 tollfree. Case report sunct syndrome successfully treated with the. Indeed, an observation period of more than 5 years speaks against a symptomatic etiology of sunct in these cases. This study was designed to evaluate the efficacy of gabapentin gbp in the treatment of shortlasting unilateral neuralgiform headache with conjunctival injection and tearing sunct syndrome on a relatively large sample of persian patients. Pareja and sjaastad, 1997, although only in small series.
The problem of shortlasting unilateral neuralgiform headache attacks with conjunctival injection and tearing sunct and shortlasting unilateral neuralgiform headache attacks with cranial autonomic symptoms suna management remains unsolved. Shortlasting unilateral neuralgiform headache mafiadoc. Visit our project page if youre interested in joining. Shortlasting unilateral neuralgiform headache attacks with conjunctival injection and tearing sunct is a primary headache syndrome. Lets not forget that there are 12 pairs of cranial nerves that feed in the pharengeal arches in some measure. Sunct shortlasting unilateral neuralgiform headache attacks with conjunctival injection and tearing.
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